Successful living donor liver transplantation in a cystic fibrosis patient with combined hepatocellular carcinoma and cholangiocarcinoma

Abstract

Combined hepatocellular carcinoma (HCC) and cholangiocarcinoma (CC) is a rare tumor entity. In this report, we describe a case of a young patient who developed a liver tumor in a cirrhotic liver caused by cystic fibrosis. All diagnostic findings suggested that this tumor was an HCC. We performed living donor liver transplantation. Histological examination of the tumor revealed combined HCC and CC as an incidental finding. Two years after the transplantation, the patient is in good clinical condition and is disease-free.

Keywords

Cholangiocarcinoma / cystic fibrosis / hepatocellular carcinoma / liver transplantation / liver tumor / living donation

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