Primary sclerosing encapsulating peritonitis with cryptorchidism in an older man: case report and literature review

Yeqing Chen , Zhenxiang Wang , Mingwei Han , Yiwu Liu , Zhengguang Yan , Yiyun Guo , Wei Xie , Hongyu Zhou

Rare Disease and Orphan Drugs Journal ›› 2026, Vol. 5 ›› Issue (3) : 22

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Rare Disease and Orphan Drugs Journal ›› 2026, Vol. 5 ›› Issue (3) :22 DOI: 10.20517/rdodj.2025.79
Case Report
Primary sclerosing encapsulating peritonitis with cryptorchidism in an older man: case report and literature review
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Abstract

We report a case of primary sclerosing encapsulating peritonitis (SEP) in a 70-year-old male, initially presenting as recurrent incomplete intestinal obstruction. Concomitant cryptorchidism was consistent with an underlying developmental cause. The patient also had subclinical type A atrophic gastritis and hypothyroidism. The diagnosis of primary SEP requires the exclusion of secondary causes and relies on a synthesis of imaging, surgical, and pathological findings. The patient underwent successful surgical intervention, including adhesion lysis and partial ileocecal resection, resulting in symptomatic relief and a favorable recovery. Primary SEP is a rare condition with non-specific symptoms, predominantly intestinal obstruction, making preoperative diagnosis difficult and misdiagnosis common. Heightened awareness and meticulous imaging analysis are essential for timely and accurate diagnosis.

Keywords

Intestinal obstruction / sclerosing encapsulating peritonitis / cryptorchidism / type A atrophic gastritis / subclinical hypothyroidism

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Yeqing Chen, Zhenxiang Wang, Mingwei Han, Yiwu Liu, Zhengguang Yan, Yiyun Guo, Wei Xie, Hongyu Zhou. Primary sclerosing encapsulating peritonitis with cryptorchidism in an older man: case report and literature review. Rare Disease and Orphan Drugs Journal, 2026, 5 (3) : 22 DOI:10.20517/rdodj.2025.79

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