Ectomesenchymal chondromyxoid tumor: a comprehensive updated review of the literature and case report

Abstract

With the aim of deepening clinical understanding, researchers have conducted a bilingual literature review of a rare oral tumor. Due to its scarcity, relatively few instances of ectomesenchymal chondromyxoid tumor (ECT) exist in English and German medical literature, yet differentiation from other oral tumors remains important. This, combined with the presentation of a new patient with an especially rare form of the disease, led Astrid Truschnegg and her team of scientists from Austria’s Medical University Graz and IMAH to compile and assess the research conducted on ECT. The team searched papers published up to late-2016 and identified proteins commonly expressed by ECTs, patterns of cellular and tissue structure, genetic similarities, as well as a shared embryonic origin of tumor-associated cells. This review offers clinicians and researchers an accessible brief of current knowledge on a rare, yet significant oral disease.

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