True hermaphroditism: A nightmare for an adult

Abstract

The disorder of sex development is a rare disorder that usually occurs in early childhood. As adults, those with disorder of sexual development present with gynecomastia, primary amenorrhea, and primary infertility, which often causes great psychological impact. We report a unique case of a male adult hermaphrodite presenting with hematometra and hematosalpinx. Early management including psychiatry counseling, gender reassignment, and surgery is essential. Our patient underwent müllerian tissue removal with phallus reconstruction.

Keywords

Disorders of sexual development / True hermaphrodite / Hematometra / Hematosalpinx

Acknowledgments

None.

Statement of ethics

This study was approved by institutional ethics committee. The participant has provided written informed consent for publication in this study. All procedures performed in this study involving human participants were in accordance with the ethical standards of the institutional and national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.

Conflict of interest statement

No conflict of interest has been declared by the authors.

Funding source

None.

Author contributions

RBV, VAG, VS, SS: Definition of intellectual content, data acquisition, manuscript preparation, manuscript editing, manuscript review;

RBV, VAG, VS: Concepts;

RBV, VAG: Design, literature search, guarantor.

Data availability

The datasets generated during and/or analyzed during the current study are available from the corresponding author on reasonable request.

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