Clinical variants of upper limbs deformities in children with arthrogryposis multiplex congenita

Abstract

From 2004 to 2012 the authors examined and treated 207 patients with upper limb deformities due to AMC. The age of children with AMC was from 5 months till 18 years. All upper limbs deformities due to AMC were deviated into 2 groups: isolated and complex forms. The isolated forms differ from each other by the level of damage of the spinal cord. There are 4 variants of isolated form with different clinical presentations (C_6-7, C_5-7, C₅-T₁, С₆). The complex form presents AMC in combination with other pathology: Erb’s palsy, cerebral palsy and congenital upper limbs anomalies. The identification variants of upper limbs deformities in patients with AMC help to choose the optimal variant of treatment and predict the results of treatment.

References

[1] Bayne L.G. Hand assessment and management of arthrogryposis multiplex congenita. Clin. Orthop. 1985;(194):68-73.

[2] Bevan W.P., Hall J.G., Bamshad M., Staheli L.T., Jaffe K.M., Song K. Arthrogryposis multiplex congenita (amyoplasia): an orthopaedic perspective. J. Pediatr. Orthop. 2007; 27(5):594-600.

[3] Brown L.M., Robson M.J., Sharrard W.J. The pathophysiology of arthrogryposis multiplex congenita neurologica. J. Bone Joint Surg. Br. 1980; 62(3):291-296.

[4] Ezaki M. Treatment of the upper limb in the child with arthrogryposis. Hand Clin. 2000;16 (4):703-711.

[5] Gibson D.A., Urs N.D. Arthrogryposis multiplex congenita. J. Bone Joint Surg. Br. 1970Aug;52(3):483-493.

[6] Mennen U., Van Heest A., Ezaki M.B., Tonkin M., George G. Arthrogryposis multiplex congenita. J. Hand Surg. Br.2005; 30(5):468-474.

[7] Smith R.J., Lipke R.W. Treatment of congenital deformities in arthrogrypotics. Plast. Reconstr. Surg. 1965; 36(4): 459.

[8] Van Heest A., Waters P.M., Simmons B.P. Surgical treatment of arthrogryposis of the elbow. Journal of Hand Surgery.1998; 23 (6):1063-1070.

[9] Weeks P.M. Surgical correction of upper extremity deformities in arthrogrypotics. Plast. Reconstr. Surg. 1965;36(4):459-465.