Harlequin’s face — a rare form of autonomic dysfunction during dissection of the internal carotid artery

Vladimir V. Belopasov , Maria V. Gubanova , Anastasia V. Belopasova , Ludmila A. Kalashnikova , Larisa A. Dobrinina

Journal of Clinical Practice ›› 2019, Vol. 10 ›› Issue (1) : 88 -93.

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Journal of Clinical Practice ›› 2019, Vol. 10 ›› Issue (1) : 88 -93. DOI: 10.17816/clinpract10188-93
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Harlequin’s face — a rare form of autonomic dysfunction during dissection of the internal carotid artery

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Abstract

A comprehensive examination and dynamic observation of a patient with clinical manifestations of connective tissue dysplasia and dissection of the internal carotid arteries revealed a symptom complex characteristic of Harlequin syndrome. The description of this form of pathology is given for the first time in the national literature. A brief review presents the diagnostic criteria and mechanisms for the development of this rare autonomic dysfunction.

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connective tissue dysplasia, carotid artery dissection, autonomic nervous system, Harlequin syndrome

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Vladimir V. Belopasov,Maria V. Gubanova,Anastasia V. Belopasova,Ludmila A. Kalashnikova,Larisa A. Dobrinina. Harlequin’s face — a rare form of autonomic dysfunction during dissection of the internal carotid artery. Journal of Clinical Practice, 2019, 10(1): 88-93 DOI:10.17816/clinpract10188-93

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Belopasov V.V., Gubanova M.V., Belopasova A.V., Kalashnikova L.A., Dobrinina L.A.

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