Harlequin’s face — a rare form of autonomic dysfunction during dissection of the internal carotid artery

Abstract

A comprehensive examination and dynamic observation of a patient with clinical manifestations of connective tissue dysplasia and dissection of the internal carotid arteries revealed a symptom complex characteristic of Harlequin syndrome. The description of this form of pathology is given for the first time in the national literature. A brief review presents the diagnostic criteria and mechanisms for the development of this rare autonomic dysfunction.

Keywords

connective tissue dysplasia, carotid artery dissection, autonomic nervous system, Harlequin syndrome

References

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RIGHTS & PERMISSIONS

Belopasov V.V., Gubanova M.V., Belopasova A.V., Kalashnikova L.A., Dobrinina L.A.