ETIOLOGY AND PATHOPHYSIOLOGY OF CHRONIC INTESTINAL SYNDROME OF PSEUDO-OBSTRUCTION IN CHILDREN Part II. Primary and secondary chronic syndrome of pseudo-obstruction in children and adults

Abstract

Chronic intestinal syndrome of pseudo-obstruction is a rare syndrome manifested through recur-rent phenomena of bowel obstruction developed against neuropathies, myopathies and neuromyo-pathies of congenital or acquired genesis. The article deals with the peculiarities of ethiopathogen-esis of different forms of the disease including de nova mutations revealed within the last decades. The article is interesting both for surgeons who must diagnose intestinal pseudo-obstruction in a timely manner to avoid unnecessary surgeries and for other doctors who can come across the syndrome during their practice.

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Averyanova Y.V., Razumovsky A.Y., Stepanov A.E.