Congenital hypertrophy of the retinal pigment epithelium

Abstract

Congenital hypertrophy of the retinal pigment epithelium is a benign pigmented lesion of the posterior pole with a unique clinical appearance. It is flat, round, and has sharp edges. While it is usually black, it may have internal lacunae without pigment. The lesion may also be all hypopigmented. Over many years, the lesions may grow slightly and change their pigmentation. Even though malignant transformation is extremely rare, annual examinations should be performed.

Keywords

congenital hypertrophy of the retinal pigment epithelium / Nevus / Pigmented retinal lesion / melanocytoma

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RIGHTS & PERMISSIONS

Cherney E.