The specific clinical and functional features of congenital aniridia with a concomitant pathology

L. A Katargina; Ekaterina Viktorovna Mazanova; A. O Tarasenkov

doi:10.17816/rpoj37653

Russian Pediatric Ophthalmology ›› 2015, Vol. 10 ›› Issue (3) : 21 -23. DOI: 10.17816/rpoj37653

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The specific clinical and functional features of congenital aniridia with a concomitant pathology

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Abstract

The results of the comprehensive ophthalmological and general somatic examination of 26 children (49 eyes) presenting with congenital aniridia have demonstrated the combination of various pathologies in the anterior and posterior segments of the eye in the majority of the patients (92.3%) including glaucoma (73.0% of the children), congenital cataract (19,2% of the children), corneal opacity (46.1% of the children), hypoplasia of the retina and optic disk (15.3% of the children), and other problems. The characteristic anatomical and functional features of the affected eyes has been revealed along with the disposition of the examined children to developing postoperative complications that need to be taken into consideration for the correct diagnosis and prognosis of a given pathology, the choice of the adequate strategies for the treatment and the long-term follow up of the children presenting with congenital aniridia.

Keywords

congenital aniridia / congenital glaucoma / congenital cataract / cornea opacity / hypoplasia of the macula and the optic disk / trabeculectomy / cataract extraction

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L. A Katargina, Ekaterina Viktorovna Mazanova, A. O Tarasenkov. The specific clinical and functional features of congenital aniridia with a concomitant pathology. Russian Pediatric Ophthalmology, 2015, 10(3): 21-23 DOI:10.17816/rpoj37653

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