Ocular manifestations of Bloch-Sulzberger syndrome
L. V Kogoleva , M. V Belova , E. N Demchenko , A. O Tarasenkov
Russian Pediatric Ophthalmology ›› 2014, Vol. 9 ›› Issue (2) : 9 -13.
Ocular manifestations of Bloch-Sulzberger syndrome
Clinical examination data of three various ages children with Bloch-Sulzberger syndrome ophthalmic manifestations are presented. It was found that this ocular pathology detects in early postnatal age and manifests with the presence of peripheral retinal avascular zones and retinal vessels changes. The long-term ophthalmic manifestation of the syndrome may have different clinical changes, various clinical and functional outcome that determines the necessity for compulsive ophthalmological examination in the early stages and dispensary observation of children with Bloch-Sulzberger syndrome.
Bloch-Sulzberger syndrome / children / hereditary diseases / retinal detachment
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