Staged correction of multiple congenital malformations

Abstract

Introduction. The authors present their own clinical observation of staged surgical correction of multiple congenital malformations in patient A. from her neonatal period up to the age of 1 year 4 months.

Clinical observation. After a comprehensive examination and staged correction of congenital malformations, the surgeons made a final stage of surgical correction of esophageal atresia - delayed esophago-esophagoanastomosis. The postoperative period was complicated by failure and stenosis of the esophageal anastomosis. After conservative therapy and bougienage of the esophagus, the patient was discharged from the hospital in a satisfactory state.

Conclusion. A favorable outcome was seen in a newborn girl with multiple congenital malformations due to timely diagnostics in the postnatal period and staged surgical correction. The authors also describe the algorithm of diagnostics and management of this patient. The obtained results have motivated the researchers to make a conclusion that step-by-step correction of multiple congenital malformations can bring good results

Keywords

esophageal atresia / thoracoscopy / esophago-esophagoanastomosis / children

References

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