FIBRO-ADIPOSE VASCULAR ANOMALY IS A NEW DIAGNOSIS IN THE PRACTICE OF A PEDIATRIC VASCULAR SURGEON. EXPERIENCE IN DIAGNOSTICS AND TREATMENT
A. G. Narbutov , M. N. Sukhov , I. I. Serkov , R. V. Garbuzov , I. S. Kletskaya
Russian Journal of Pediatric Surgery ›› 2020, Vol. 24 ›› Issue (1) : 11 -15.
FIBRO-ADIPOSE VASCULAR ANOMALY IS A NEW DIAGNOSIS IN THE PRACTICE OF A PEDIATRIC VASCULAR SURGEON. EXPERIENCE IN DIAGNOSTICS AND TREATMENT
The article discusses results of surgical treatment of 25 children, aged 1 to 14, with fibro-adipose vascular anomaly (FAVA) of lower extremities. The patients were treated in Pirogov Russian Pediatric Clinical Hospital in 2015-2019. Diagnostic findings are presented; basic features of the discussed pathology are described. As the obtained results have shown, in the authors’ opinion, the discussed surgical approach turned to be quite effective, since it significantly improves the quality of life, and in some cases brings complete disappearance of complaints and symptoms in patients with FAVA.
vascular malformations / fibro-adipose vascular anomaly / pediatric vascular surgery
| [1] |
Alomari, A.I., et al., Fibro-adipose vascular anomaly: clinical-radiologic-pathologic features of a newly delineated disorder of the extremity. J Pediatr Orthop, 2014; 34(1): 109-17. |
| [2] |
Fernandez-Pineda, I., et al., Lower Extremity Fibro-Adipose Vascular Anomaly (FAVA): A New Case of a Newly Delineated Disorder. Ann Vasc Dis, 2014: 7(3): 316-9. |
| [3] |
Clemens, R.K., et al., Combined and complex vascular malformations. Vasa, 2015. 44(2): 92-105. |
| [4] |
Erickson, J., et al., Fibroadipose vascular anomaly treated with sirolimus: Successful outcome in two patients. Pediatr Dermatol. 2017. 34(6): 317-320. |
| [5] |
Johnson, C.M. and O.M. Navarro, Clinical and sonographic features of pediatric soft-tissue vascular anomalies part 2: vascular malformations. Pediatr Radiol, 2017. 47(9): 1196-1208. |
| [6] |
Luks, V.L., et al., Lymphatic and other vascular malformative/overgrowth disorders are caused by somatic mutations in PIK3CA. J Pediatr, 2015. 166(4): 1048-54 e1-5. |
| [7] |
Ramaswamy, R.S., et al., Cryoablation of low-flow vascular malformations. Diagn Interv Radiol, 2019. 25(3):225-230. |
| [8] |
Shaikh, R., et al., Cryoablation in fibro-adipose vascular anomaly (FAVA): a minimally invasive treatment option. Pediatr Radiol, 2016. 46(8): 1179-86. |
| [9] |
Sheybani, E.F., E.P. Eutsler, and O.M. Navarro, Fat-containing soft-tissue masses in children. Pediatr Radiol, 2016. 46(13): 1760-1773. |
| [10] |
Wang, K.K., et al., Surgical Management of Fibroadipose Vascular Anomaly of the Lower Extremities. J Pediatr Orthop, 2019. |
| [11] |
Domb BG, Khanna AJ, Mitchell SE, et al. Toe-walking attributable to venous malformation of the calf muscle. Clin Orthop. 2004;420:225-229. |
| [12] |
Klemme WR, James P, Skinner SR. Latent onset unilateral toe- walking secondary to hemangioma of the gastrocnemius. J Pediatr Orthop. 1994; 14: 773-775. |
| [13] |
Wu JL, Wu CC, Wang SJ, et al. Imaging strategies in intramuscular haemangiomas: an analysis of 20 cases. Int Orthop. 2007; 31: 569-575 |
| [14] |
Wang YC, Jeng CM, Wu DY, et al. Giant ossified cavernous hemangioma of an extremity associated with an equinovarus deformity. Skeletal Radiol. 1998; 27: 522-524. |
/
| 〈 |
|
〉 |