A CLINICAL CASE OF THE IDIOPATHIC SUPERFICIAL SIDEROSIS OF THE CENTRAL NERVOUS SYSTEM

Abstract

There was presented a clinical case of a patient with superficial siderosis of the central nervous system. The presence of the clinical triad (sensorineural hearing loss, cerebellar ataxia, pyramidal symptoms), a progressive course of the disease and characteristic neuroimaging features (MRI in T2-gradient echo and SWI - Susceptibility-Weighted Imaging - MRI images, weighted by the inhomogeneity of the magnetic field) in the form of hemosiderin deposits has allowed to establish the diagnosis.

Keywords

superficial siderosis of the Central nervous system / sensorineural hearing loss / cerebellar ataxia / pyramidal symptoms / hemosiderin

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RIGHTS & PERMISSIONS

Klocheva E.G., Goldobin V.V., Timonina O.I.