Caroli's disease with multiple cholangiogenic abscesses of left liver lobe: a clinical case

Abstract

To analyze the methods of diagnostics, treatment and outcomes of Caroli disease. The medical history, diagnostic methods and treatment of a patient with a clinical diagnosis of Caroli's disease were studied on the basis of the Surgical Department of the First Republican Clinical Hospital in Izhevsk. The results of the study showed that the final clinical diagnosis was made on the basis of the following: complaints, disease development, instrumental and laboratory diagnostic data. A timely surgical intervention, combined with all diagnostic methods, identified a rare and difficult clinical diagnosis – Caroli’s disease. In the presented clinical case, after collecting anamnesis and conducting studies, a diagnosis of a rare Caroli’s disease was made and a planned operation was performed. A regular monitoring of X-ray examinations, biochemical blood tests, and a timely medical care provide a favorable prognosis – long-term remission. In case of complications, there is a high risk for the development of biliary cirrhosis.

Keywords

Caroli's disease / intrahepatic cholangiolithiasis / left hemihepatectomy / reconstructive plastic surgery of common hepatic duct on Kera frame drainage

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