Connective tissue dysplasia in surgery

Abstract

Objective. To identify the features of connective tissue dysplasia in patients undergoing treatment in the Surgical Unit of the First Republican Clinical Hospital of Izhevsk.

Materials and methods. The study of connective tissue pathology was conducted in patients with surgical diseases on the basis of the Surgical Unit of the "First Republican Clinical Hospital of the Ministry of Healthcare of the Udmurt Republic".

Results. The following phenotypic manifestations of connective tissue dysplasia were revealed in the examined patients: asthenic type of constitution; body weight deficiency; dolichostenomelia; arachnodactyly; deformities of the chest and spine; joint mobility; atrophic striae, skin hyperextension; longitudinal and transverse flat feet; ventral and inguinal hernias; varicose veins.

Conclusions. Thus, the variety of clinical symptoms in connective tissue pathology indicates the systemic nature of the lesion since connective tissue is located in almost all organs and systems and has a number of important functions. In its turn, underestimating the importance of connective tissue dysplasia leads to the development of severe complications, which require early diagnosis, timely prevention, and, if necessary, adequate complex therapy and rehabilitation of patients with this syndrome.

Keywords

connective tissue dysplasia / surgery / surgical patients / clinical case

References

[1] Styazhkina S.N., Chernyshova T.E., Zykina S.A. Connective tissue dysplasia: modern ideas about etiopathogenesis, classification, clinical picture, principles of treatment and prevention, educational and methodical manual. Edited by Prof. S.N. Styazhkina. Izhevsk 2015; 44–52 (in Russian).

[2] Стяжкина С.Н., Чернышова Т.Е., Зыкина С.А. Дисплазия соединительной ткани: современные представления об этиопатогенезе, классификации, клинической картине, принципы лечения и профилактики: учебно-методическое пособие. Под ред. проф. С.Н. Стяжкиной. Ижевск 2015; 44–52.

[3] Butolin E.G., Chernyshova T.E., Ivanova I.L. edited by Prof. T.E. Chernyshova. Neurological aspects of connective tissue dysplasia: diagnosis, treatment, rehabilitation: uch-method. stipend. Izhevsk 2012; 10–17 (in Russian).

[4] Бутолин Е.Г., Чернышова Т.Е., Иванова И.Л. Неврологические аспекты дисплазии соединительной ткани: диагностика, лечение, реабилитация: уч-метод. пособие. Под ред. проф. Т.Е. Чернышовой. Ижевск 2012; 10–17.

[5] Connective tissue Dysplasia: The clinical recommendations of the RNMOT. Were approved at the XII National Congress of Therapists on November 22–24, 2017. Moscow 2017 (in Russian).

[6] Дисплазии соединительной ткани: клинические рекомендации РНМОТ. Утверждены на XII Национальном конгрессе терапевтов 22–24 ноября 2017 года. М. 2017.

[7] Connective tissue dysplasia. Edited by T.I. Kadurina, V.N. Gorbunova. St. Petersburg: Albi 2009; 714 (in Russian).

[8] Дисплазия соединительной ткани. Под ред. Т.И. Кадуриной, В.Н. Горбуновой. СПб.: Элби 2009; 714.

[9] Kuzmin M.I., Shkrob O.S., Kuzin N.M. et al. Surgical diseases: text-book. Edited by M.I. Kuzin. 3rd ed., reprint. and additional. Moscow: Medicine 2002; 784 (in Russian).

[10] Кузьмин М.И., Шкроб О.С., Кузин Н.М. и др. Хирургические болезни: учебник. Под ред. М.И. Кузина. 3-е изд., перераб. и доп. М.: Медицина 2002: 784 с.

[11] Styazhkina S.N., Salamatov A.Yu., Ogoreltseva L.S., Salimova G.R., Semenov Yu.V. Connective tissue dysplasia as a marker of postoperative complications in herniation. Collection of articles of the IV International Scientific and Practical Conference "Actual problems of science of the XXI century". 2015; 2 (in Russian).

[12] Стяжкина С.Н., Саламатов А.Ю., Огорельцева Л.С., Салимова Г.Р., Семенов Ю.В. Дисплазия соединительной ткани как маркер послеоперационных осложнений при грыжесечении. Актуальные проблемы науки XXI века: сборник статей IV Международной научно-практической конференции. 2015; 2.

[13] Nechaeva G.I., Yakovlev V.M., Konev V.P. et al. Connective tissue dysplasia: basic clinical syndromes, diagnosis formulation, treatment. Attending physician 2008; 2: 22–28 (in Russian).

[14] Нечаева Г.И., Яковлев В.М., Конев В.П. и др. Дисплазия соединительной ткани: основные клинические синдромы, формулировка диагноза, лечение. Лечащий врач 2008; 2: 22–28.

RIGHTS & PERMISSIONS

styazhkina S.N., Capustin B.B., Malchicov A.Y., Chernyshova T.E., Kononova N.Y., Usachev A.V., Shisterova E.V.