Clinical case of granulomatosis with polyangiitis (Wegener’s) with isolated pulmonary lesion
Oksana V. Obukhova , Olga V. Khlynova
Perm Medical Journal ›› 2019, Vol. 36 ›› Issue (4) : 82 -87.
Clinical case of granulomatosis with polyangiitis (Wegener’s) with isolated pulmonary lesion
Pulmonary vasculites include geterogenic group of diseases, characterized by destruction of pulmonary vessels with inflammation and tissue necrosis. From the clinical point of view, pulmonary vasculites are still difficult to diagnose and treat.
Pulmonary lesion is one of typical features of granulomatosis with polyangiitis (GPA) along with upper respiratory tract and renal pathologies, composing classical triad of this disease.
In case of GPA, pulmonary lesion is diagnosed in 60–85 % of patients. As a rule, it is combined with involvement of other organs, but in 9 % of patients, it can be the main manifestation of disease. The paper presents a case of GPA with isolated pulmonary lesion.
Pulmonary vasculitis / granulomatosis with polyangiitis / ANCA-associated vasculitis
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Obukhova O.V., Khlynova O.V.
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